Patel Plastic Surgery Salt Lake City and St. George
  • Home
  • Locations
    • Plastic Surgery Salt Lake City
    • Plastic Surgery St. George
  • Conditions
    • Aging Of The Face
    • Aging of Lower Eyelids
    • Aging of the Forehead and Brows
    • Aging of Upper Eyelids
    • Aging of the Cheeks
    • Aging of the Neck
    • Aging of the Lips
    • Aging of the Mouth
    • Aging of the Chin
    • Aging of Eyelashes
    • Aging of the Hands
    • Aging Of Skin Colour
    • Aging Of Hair
    • Aging of the Jowls
    • Aging of Men
    • Aging of the Skin
    • Aging of Veins and Vessels
    • Scars
  • Cosmetic
    • Facelift
    • Browlifts
    • Lower Blepharoplasty
    • Upper Blepharoplasty
    • Midface Lift/Hammock Lift
    • Necklift
    • Cosmetic Surgery for Men
    • Lip Lines
    • Lips
    • Mouth
    • Neck Liposuction
    • Fat Transfer
    • Skin Resurfacing
    • Cheeks
    • J-PLASMA SKIN RESURFACING
    • J-PLAZTY FACE
    • Removal of Moles, Lesions, Tags, Cysts and Blemishes
    • Facial Implants
    • Otoplasty, Ear Pinning, or Bat-Ear Repair
    • Complications?
  • Reconstruction
    • Acquired Ptosis and Dermatochalasis
    • Congenital Ptosis
    • Ptosis in Myasthenia Gravis
    • Blepharophimosis Syndrome
    • Entropion
    • Ectropion
    • Thyroid Eye Disease
    • Nasolacrimal Duct Obstruction
    • Skin Tumors
    • Orbital Tumors
    • Blepharospasm
    • Pterygium
    • Anophthalmos and Microphthalmos
    • Enucleation and Evisceration
    • Exenteration
    • Symblepharon
    • Congenital Anomalies - Lid Disorders
    • Acne Rosacea
    • Trauma
    • Infections
  • Non Invasive
    • Photorejuvenation
    • Aerolase Laser
    • Botox
    • Radiesse
    • Restylane
    • Juvederm
    • Fractional Carbon Dioxide CO2 Laser
    • Fractional Resurfacing Lasers: Erbium lasers
    • Laser Hair Removal
    • Kybella
    • Chemical Peels
    • XEOMIN ®
    • Voluma
    • LATISSE EYELASH TREATMENT
    • Leg Veins and Spider Vein Treatment
    • Sculptra
    • Neck and Chest Cosmetic Concerns
    • Dysport
    • Accent Radiofrequency
    • Microdermabrasion and Light Chemical Peels
    • Melasma
    • Laser Tattoo Removal
    • Color and Texture Issues – Brown Spots on Face, Redness
    • Scars and Acne
    • Permanent Cosmetic Makeup
  • Resources
    • Patient Forms & Downloads
    • Out Of State and Overseas Patients
    • Reviews
    • VIDEOS Patel Plastic Surgery
  • About
  • Blog
  • Contact

blepharophimosis syndrome (BPES)

To read a blepharophimosis chapter by Prof BCK Patel MD, FRCS published in a textbook, please read below

To download a blepharophimosis chapter by Prof BCK Patel MD, FRCS published in a textbook, please download here 

Download

What is blepharophimosis syndrome?
Blepharophimosis is from the Greek blepharon (eyelid), and phimosis (stricture).

Blepharophimosis Syndrome is also known as the Blepharophimosis, Ptosis, Epicanthus inversus Syndrome, usually abbreviated as "BPES"

Blepharophimosis Syndrome causes the palpebral aperture to be small both, horizontally and vertically. It may be associated with a variety of other condition.​
Blepharophimosis photograph showing autosomal dominant feature by Prof. BCK Patel MD, FRCS
Autosomal Dominant Blepharophimosis Syndrome with blepharophimosis, ptosis and epicanthus inversus

blepharophimosis syndrome (BPES)


Blepharophimosis Syndrome is now known to have the following findings:
  • Blepharophimosis
  • Ptosis
  • Epicanthus Inversus
  • Telecanthus (added to the syndrome by Kohn and Romano): long medial canthus which reduces the horizontal fissure from the normal 25 - 30 mm to as little as 20 mm
  • Hypoplasia of the tarsal plates
  • Lengthening of the lateral canthal tendon
  • Epiblepharon
  • Lower eyelid retraction
  • Eyelid ectropion
  • Flat supraorbital rim
  • Punctal anomalies
  • Female infertility may occur
  • Amblyopia may be found in more than 50% of patients
  • Strabismus is found in 26.7%
  • Gene localization studies indicate that the location of the blepharophimosis gene is at 3q2
“Fortunately, for us, Dr. Patel at Primary Children’s Hospital – Moran Eye Center, was equally comforting as he was qualified. He has phenomenal bedside manners, and is an extremely kind human being. Nothing about our experience with him made us feel like he was in a routine, or that he’d seen this a thousand times, he treated us as friends, and as if he was bearing this burden with us.”
Parents of child with Blepharophimosis Syndrome, USA
​
Schedule Your Consult


​when was blepharophimosis first described?

Although the condition of blepharophimosis (small apertures of the eyelids) was first described by von Ammon in 1841, the SYNDROME of Blepharophimosis was described as a triad consisting of blepharophimosis, ptosis and epicanthus inversus by Komoto in 1921.

​Dimitry, also in 1921, coined the term "Blepharophimosis" when de described a family with the condition and he was the first to note the dominant inheritance of this condition.




​
Blepharophimosis Syndrome with severe ptosis, phimosis, telecanthus and chin-up position adopted by the child to see. Photo by Prof. BCK Patel MD, FRCS
Blepharophimosis syndrome with marked phimosis, severe ptosis and chin-up position adopted by the child
Blepharophimosis photograph showing autosomal dominant feature by Prof. BCK Patel MD, FRCS
Autosomal Dominant Blepharophimosis Syndrome with dad and both children affected

management of Blepharophimosis syndrome

Most children with the Blepharophimosis Syndrome will have a ptosis (droopy upper eyelids) with poor levator function. The following will be seen:
  1. A chin-up position will be adopted by the child as the eyelids interfere with vision
  2. The upper eyelids will not have a crease because of the poor levator function
  3. The child will actively raise the brows in order to indirectly raise the upper eyelids
  4. The whole eye opening will look smaller because of the ptosis, the phimosis and the telecanthus
Because the risk of amblyopia is high, we perform a frontalis sling early (see photos below). As the child is not big enough to allow us to use fascia lata from the leg, temporary materials like goretex or silicone are used to perform the slings: in our hands, these slings work very well and last for many years. 

​Once the child is older, and when the more permanent slings need to be performed, we use autogenous fascia lata to lift tye lids. 


Blepharophimosis syndrome repair with frontalis slings by Prof. BCK Patel MD, FRCS
Blepharophimosis Syndrome with severe ptosis and phimosis and telecanthus. Photos after frontalis slings to allow visual development. The telecanthus repair will be performed when the child is older to give the best cosmetic results
"Why don't we have more doctors like this doctor? He really knows his stuff but he is also very patient and explains things clearly.

I had botched surgery and had too many operations (five). Every time someone would see me they would want to operate and I was always left worse off. I finally was very frustrated and did not want to come from Montana and drive 8 hours just to see yet another doctor but I am so glad I did. My eyes are so much more comfortable now after Dr. Patel's care and I even look better. He took his time analyzing all my procedures and planning things and I will always be grateful to him and to the University for having this great doctor.


W.E  53 Yrs Old with "trouble until I came here!"- Billings, MT
​

total management of blepharophimosis syndrome

The sequence of repair is to perform the droopy-eyelid surgery with frontalis slings as soon as possible, followed by repair of the telecanthus some years later once the nasal bridge has developed somewhat.

​Over time, the slings will relax. In the beginning (immediately after surgery), it is understandable that parents will be surprised to see the eyelids wide open and even open when the child sleeps: this relaxes and, fortunately, does not seem to bother our children. However, we will give you simple instructions so that the corneas may be kept lubricated. This applies to all frontalis sling procedures, whether performed in children with the Blepharophimosis Syndrome or with severe congenital ptosis
Blepharophimosis Syndrome repair by Prof. BCK Patel with repair of the ptosis with frontalis slings, repair of the lower lid retraction and cheek ptosis and telecanthus using the modified Patel technique to give minimal scarring
Blepharophimosis Syndrome with severe ptosis and phimosis and telecanthus. Photos after frontalis slings to allow visual development and repair of the telecanthus. The lower eyelid retraction and cheek ptosis have also been repaired

How is Congenital Ptosis with poor levator function repaired?

Dr. Patel uses the "micro-incision" approach to insertion of frontalis slings so the scarring is minimal. Indeed, most parents cannot see our scars after a few months (see photos above and below). Similarly, when repairing the telecanthus, the lateral canthal malposition and the cheek hypoplasia, cosmetic principles are applied to give gratifying results
Blepharophimosis Syndrome repair by Prof. BCK Patel with repair of the ptosis with frontalis slings, repair of the lower lid retraction and cheek ptosis and telecanthus using the modified Patel technique to give minimal scarring
Careful followup and repair of the different structures yields excellent results in the Blepharophimosis Syndrome. The old medial canthoplasties used to leave patients with extensive scars even though they corrected the telecanthus, so Dr. Patel uses the technique he designed and applying cosmetic principles to this surgery, excellent results are obtained
Picture
Picture
Picture
Picture
Picture
Picture
Picture

Frontalis Sling

When the weakness is profound, with little or no function, “frontalis slings” are performed. Before a child is 4 or 5 years old, temporary materials are used to elevate the eyelids so that vision may develop more normally.

​When the child is older, fascia lata is obtained from the leg to perform slings. The fascia lata slings last much longer as the material is autogenous.
Picture
Blepharophimosis repair with fascia lata frontalis slings by Prof. BCK Patel MD, FRCS of Salt Lake City and St. George, Utah and London, England
Accurate measurements and markings of palpebral fissures and telecanthus to design the repair of the canthal tendons after the fascia lata frontalis slings have been inserted
Picture
Blepharophimosis repair with fascia lata frontalis slings by Prof. BCK Patel MD, FRCS of Salt Lake City and St. George, Utah and London, England
Obtaining fascia lata for performing fascia lata slings
Blepharophimosis repair with fascia lata frontalis slings by Prof. BCK Patel MD, FRCS of Salt Lake City and St. George, Utah and London, England
Fascia lata slings being inserted to give a good upper eyelid height as well as curve
Frontalis slings with fascia lata and Patel modified medial canthoplasties for the Blepharophimosis syndrome
Frontalis slings with fascia lata and Patel modified medial canthoplasties for the Blepharophimosis syndrome
Blepharophimosis repair with fascia lata frontalis slings by Prof. BCK Patel MD, FRCS of Salt Lake City and St. George, Utah and London, England
Design and placement of the frontalis slings for repair of the ptosis with poor levator function
Blepharophimosis repair with fascia lata frontalis slings by Prof. BCK Patel MD, FRCS of Salt Lake City and St. George, Utah and London, England
After the insertion of the fascia lata frontalis slings, the medial canthal region is measured and marked
Blepharophimosis repair with fascia lata frontalis slings by Prof. BCK Patel MD, FRCS of Salt Lake City and St. George, Utah and London, England
Repair of the telecanthus involves work on the long medial canthal tendon as well as repair of the epicanthus inversus

Before and After photographs after use of frontalis slings in children and adults 

Picture
Picture
Picture
Picture
Picture
Picture
Picture
Picture
"I had a excellent eye lift done by Dr. Patel. He knows what he is doing and is very pleasant. Dr.Patel was easy to get an appointment and he works with you. The office staff was very pleasant and made you feel calm."  D. Gull Highly recommended for eye lift surgery - Salt Lake City, UT

Will the frontalis sling ptosis surgery need to be repeated?

The initial frontalis slings use goretex or silicone material and last for a number of years. Once the child is five years or older and if the lids droop again, then fascia lata slings are performed. These last for many decades. Even when the child has essentially no levator function, we are able to design a very attractive upper eyelid and crease. Small asymmetries will remain as all this is "man-made"!

What care will I need to give my child after ptosis Surgery

Whether a direct levator advancement procedure is performed or a frontalis sling is performed, it is normal for the child to sleep with the eyelids somewhat open: this may be dramatic in the beginning but the degree of opening reduces over time. However, the lids may stay open to some degree for a long time or forever. This is normal and every child will experience this. After surgery, the following instructions should be followed: Incisions which are hidden in front of and behind the ear. Once healed, they are close to invisible.
  1. The incision sites will need the application of erythromycin eye ointment three times a day for about a week: this will be prescribed.
  2. It will be important to keep the incision sites clean: clean hands!
  3. Any oral antibiotics prescribed (especially important when frontalis slings are performed) must be administered.
  4. For the first few weeks, applying a small amount of eye lubricating ointment (Refresh pm ointment or any other eye lubricating ointment will do) whenever the child sleeps or takes a nap is important. After a few weeks, most children do not need continud application of ointment unless they are unwell or have a cold. We will guide you.
  5. Most children see so much better once the eyelid/eyelids have been lifted that you will notice them being much more physically active! This all to the good!
  6. If patching was prescribed by the paediatric ophthalmology team, please continue with the patching until you see the team again: they will reduce or stop the patching once appropriate.
  7. Most children can return to school within three or four days. There is very little pain after this surgery: children’s Tylenol is usually sufficient.
  8. We will monitor the eyelid height once every six to nine months; the paediatric ophthalmology team will assess visual development and examine you for any strabismus or need for patching as well.

What sort of scars will there be?

When a direct incision is made to lift the eyelid, the incision is hidden in where a natural crease would form. All children heal with a pink scar initialy, but this is almost invisible after a few months. After frontalis slings, the incisions become almost invisible within a few months as we make very small incisions using a technique that we developed at the University of Utah and have taught to surgeons from all over the world. We take pride in our “small-incision” frontalis slings with minimal scars, unlike the way the surgery is performed in many other centers. It is normal to feel small bumps under the skin after frontalis slings as the sling material is attached to the frontalis muscle:
​however, these are rarely visible.

Schedule Your Consult Today

Contact Us
"Dr.Patel such a wonderful person...trust worthy, making u feel like family, included his staff members. Made my worries go away with there caring ways. God bless them. He truly make a wonderful job...it seem like a miracle. Dr. Patel makes magic happen." -Vitals.com Visitor Review
Picture
Visit Patel Plastic Surgery on YouTube for more free tips!

Stay Connected With Us On Social Media
See All Videos >>

Find Us

Locations: 
​Dr. BCK Patel MD, FRCS
​1025E 3300S
Salt Lake City, Utah 84106, USA

(801) 413-3599 (phone/text)
E: [email protected]
bckpatel.info

Dr. BCK Patel MD, FRCS
617 E Riverside Dr Suite 101
​Saint George, UT 84790, USA
(435) 215-0014
​E: [email protected]
Quick-Link

Let Us answer your questions

Submit

Conditions

Aging Of The Face
Aging of Lower Eyelids
Aging of the Forehead and Brows
Aging of Eyelashes
Aging of the Cheeks
Aging of the Neck
Aging of the Lips
Aging of the Mouth
Aging of the Chin
Aging of Eyelashes
Aging of the Hands
Aging Of Skin Colour
Aging Of Hair
​Aging of the Jowls
Aging of Men
Aging of the Skin
Aging of Veins and Vessels
Scars

Cosmetic

Facelift
Browlifts
Lower Blepharoplasty/Hammock Lift
Upper Blepharoplasty
Midface Lift/Hammock Lift
Necklift
Lips
Mouth
Neck Liposuction
Fat Transfer
Skin Resurfacing
Cheeks
J-PLASMA SKIN RESURFACING
J-PLAZTY FACE
Removal of Moles, Lesions, Tags, Cysts and Blemishes
Facial Implants
Otoplasty, Ear Pinning, or Bat-Ear Repair
​Complications?

Reconstruction

​Entropion
Acquired Ptosis
Ectropion
Congenital Ptosis
Blepharospasm
Anophthalmos and Microphthalmos
Thyroid Eye Disease
Enucleation and Evisceration
Nasolacrimal Duct Obstruction
Symblepharon
Congenital Anomalies - Lid Disorders
Acne Rosacea
Trauma
Infections
Skin Tumors
Orbital Tumors

Non- Invasive

 Photorejuvenation
Aerolase Laser
Botox
Laser Hair Removal
Kybella
Juvederm
Chemical Peels
Fractional Carbon Dioxide CO2 Laser
XEOMIN ®
Voluma
Latisse Eyelash Treatment
Leg Veins and Spider Vein Treatment
Sculptra
Neck and Chest Cosmetic Concerns
Restylane
Dysport
Accent Radiofrequency
Microdermabrasion and Light Chemical Peels
Melasma
Fractional Resurfacing Lasers: Erbium lasers
Color and Texture Issues – Brown Spots on Face, Redness
Laser Tattoo Removal
Radiesse
Acne
​Permanent Cosmetic Makeup

VIDEOS

links
​
www.hammocklift.com

WWW.PATELFACELIFT.COM

www.englishsurgeon.com

www.drbhupendrapatel.com
​
bckpatel.info

WEBOFSCIENCE

researchgate

GOOGLE SCHOLAR

Patel Plastic Surgery  .  Copyright 2022 . All Rights Reserved
  • Home
  • Locations
    • Plastic Surgery Salt Lake City
    • Plastic Surgery St. George
  • Conditions
    • Aging Of The Face
    • Aging of Lower Eyelids
    • Aging of the Forehead and Brows
    • Aging of Upper Eyelids
    • Aging of the Cheeks
    • Aging of the Neck
    • Aging of the Lips
    • Aging of the Mouth
    • Aging of the Chin
    • Aging of Eyelashes
    • Aging of the Hands
    • Aging Of Skin Colour
    • Aging Of Hair
    • Aging of the Jowls
    • Aging of Men
    • Aging of the Skin
    • Aging of Veins and Vessels
    • Scars
  • Cosmetic
    • Facelift
    • Browlifts
    • Lower Blepharoplasty
    • Upper Blepharoplasty
    • Midface Lift/Hammock Lift
    • Necklift
    • Cosmetic Surgery for Men
    • Lip Lines
    • Lips
    • Mouth
    • Neck Liposuction
    • Fat Transfer
    • Skin Resurfacing
    • Cheeks
    • J-PLASMA SKIN RESURFACING
    • J-PLAZTY FACE
    • Removal of Moles, Lesions, Tags, Cysts and Blemishes
    • Facial Implants
    • Otoplasty, Ear Pinning, or Bat-Ear Repair
    • Complications?
  • Reconstruction
    • Acquired Ptosis and Dermatochalasis
    • Congenital Ptosis
    • Ptosis in Myasthenia Gravis
    • Blepharophimosis Syndrome
    • Entropion
    • Ectropion
    • Thyroid Eye Disease
    • Nasolacrimal Duct Obstruction
    • Skin Tumors
    • Orbital Tumors
    • Blepharospasm
    • Pterygium
    • Anophthalmos and Microphthalmos
    • Enucleation and Evisceration
    • Exenteration
    • Symblepharon
    • Congenital Anomalies - Lid Disorders
    • Acne Rosacea
    • Trauma
    • Infections
  • Non Invasive
    • Photorejuvenation
    • Aerolase Laser
    • Botox
    • Radiesse
    • Restylane
    • Juvederm
    • Fractional Carbon Dioxide CO2 Laser
    • Fractional Resurfacing Lasers: Erbium lasers
    • Laser Hair Removal
    • Kybella
    • Chemical Peels
    • XEOMIN ®
    • Voluma
    • LATISSE EYELASH TREATMENT
    • Leg Veins and Spider Vein Treatment
    • Sculptra
    • Neck and Chest Cosmetic Concerns
    • Dysport
    • Accent Radiofrequency
    • Microdermabrasion and Light Chemical Peels
    • Melasma
    • Laser Tattoo Removal
    • Color and Texture Issues – Brown Spots on Face, Redness
    • Scars and Acne
    • Permanent Cosmetic Makeup
  • Resources
    • Patient Forms & Downloads
    • Out Of State and Overseas Patients
    • Reviews
    • VIDEOS Patel Plastic Surgery
  • About
  • Blog
  • Contact